Basal Transsphenoidal Encephalocele: MR Findings
ثبت نشده
چکیده
A 15-year-old girl presented for evaluation of short stature and delayed sexual maturation. Her weight and height were 91 lb. (41 .3 kg) and 58 in. (147.3 em), respectively. She had not yet begun menstruating and had had no development of secondary sexual characteristics. Moderate ocular hypertelorism was present. A brain CT scan was initially interpreted as showing an intrasellar and suprasellar lucent nonenhancing mass (Figs. 1 A and 1 B). Subsequent MR studies (Figs. 1 C and 1 D) revealed a transsphenoidal encephalocele.
منابع مشابه
Transsellar transsphenoidal rhino-oral encephalocele.
Transsphenoidal encephaloceles are rare and the transsellar variety is the least common. We present a 1-year-old male patient with transsellar transsphenoidal encephalocele which herniated into the oral cavity through the congenital split palate. The patient was operated on using a combined transcranial and transpalatal approach without mortality or permanent morbidity. Clinical findings, imagi...
متن کاملTranssphenoidal encephalocele masquerading as nasal mass in a 2-year-old boy.
To cite: Chandran S, Raturi S, Pillay HM, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/ bcr-2013-201426 DESCRIPTION A full-term male baby was born to nonconsanguineous parents. At birth his growth parameters were appropriate for age. On examination he had hypertelorism, broad nasal root and a cleft lip. Cranial ultrasound at birth was grossly normal except f...
متن کاملBasal encephalocele associated with morning glory syndrome: case report.
The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal deficiencies may occur. We accounted for a pituitary dwarfism with delayed diagn...
متن کاملLarge Sphenoethmoidal Encephalocele Associated with Agenesis of Corpus Callosum and Cleft Palate
Basal encephalocele is a rare craniofacial anomaly. In the present paper we report a 10-year-old boy presented with cleft palate, congenital nystagmus, and hypertelorism. During preoperative evaluation for cleft palate repair, a pulsatile mass was detected in the pharynx. Magnetic resonance imaging showed sphenoethmoidal type of basal encephalocele and agenesis of corpus callosum. Neurosurgical...
متن کاملDysgenesis of the internal carotid artery associated with transsphenoidal encephalocele: a neural crest syndrome?
We describe two original cases of internal carotid artery dysgenesis associated with a malformative spectrum, which includes transsphenoidal encephalocele, optic nerve coloboma, hypopituitarism, and hypertelorism. Cephalic neural crest cells migrate to various regions in the head and neck where they contribute to the development of structures as diverse as the anterior skull base, the walls of ...
متن کامل