Loeys-Dietz syndrome with bilateral radial head dislocations: a case report.

نویسندگان

  • Tarush Rustagi
  • Mandar V Agashe
  • Jaideep Dhamele
  • Alaric J Aroojis
  • Rujuta Mehta
چکیده

Loeys-Dietz syndrome is characterised by vascular aneurysms, hypertelorism, and a bifid uvula. We report on an 11-year-old boy with Loeys-Dietz syndrome who presented with bilateral radial head dislocations and severe osteopaenia with changes of avascular necrosis in both hips causing an out-toeing, wide gait. Considering the poor prognosis for elbow movement and possible radial head dysplasia, surgical reduction of the radial heads was deferred. A subtrochanteric de-rotation osteotomy of the left hip was performed to improve the gait.

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عنوان ژورنال:
  • Journal of orthopaedic surgery

دوره 21 2  شماره 

صفحات  -

تاریخ انتشار 2013