Pulmonary lymphangioleiomyomatosis--a silent killer?
نویسندگان
چکیده
Pulmonary lymphangioleiomyomatosis (LAM) is a rare disorder presenting with remarkable features like recurrent pneumothorax or chylothorax, usually in young women. We report a case of sporadic LAM who presented with nothing but recent onset exertional dyspnoea and it was this unobtrusive presentation that led to delay in diagnosis.
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ورودعنوان ژورنال:
- The Journal of the Association of Physicians of India
دوره 60 شماره
صفحات -
تاریخ انتشار 2012