A Case of Phacomatosis Pigmentovascularis Type IIa in a Korean Infant
نویسندگان
چکیده
638 Ann Dermatol Received April 5, 2016, Revised September 7, 2016, Accepted for publication September 9, 2016 Corresponding author: Sang Seok Kim, Department of Dermatology, Kangdong Sacred Heart Hospital, Hallym University College of Medicine, 150 Seongan-ro, Gangdong-gu, Seoul 05355, Korea. Tel: 82-2-2224-2285, Fax: 82-2-474-7918, E-mail: [email protected] This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/ licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. Copyright © The Korean Dermatological Association and The Korean Society for Investigative Dermatology Fig. 1. Bilateral erythematous-violaceous nevus on the face and generalized nevus flammeus on the whole body. Bluish-gray Mongolian spots are seen on the trunk, back, buttock and extremities. https://doi.org/10.5021/ad.2017.29.5.638
منابع مشابه
Phacomatosis pigmentovascularis type IIa - Case report*
Phacomatosis Pigmentovascularis is a rare syndrome characterized by capillary malformation and pigmentary nevus. A case of a 2-year-old patient is reported, who presented extensive nevus flammeus and an aberrant Mongolian spot, without systemic disease, manifestations that allow us to classify this case as type IIa Phacomatosis Pigmentovascularis, according to Hasegawa's classification.
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