Trilateral retinoblastoma with unilateral eye involvement.

نویسندگان

  • Irfanullah Shah
  • Adnan Baig
  • Abdul Razzaq
  • Anum Faruqi
  • Aun Ali
  • Faraz Qayyum Khan
چکیده

Trilateral retinoblastoma (TRb) is a rare combination of unilateral or bilateral retinoblastoma with an ectopic midline intracranial neuroblastic neoplasm (primitive neuroectodermal tumour) usually in the area of pineal gland or sellar region. TRb can occur with both familial and sporadic forms of retinoblastoma. An occurrence of this rare tumour in a 12-year-old boy who had unilateral retinoblastoma in association with ectopic suprasellar primitive neuroectodermal tumour (PNET) is reported here. To the best of our knowledge, this is the first case report in Pakistan on TRb with suprasellar mass.

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عنوان ژورنال:
  • Revista da Associacao Medica Brasileira

دوره 61 4  شماره 

صفحات  -

تاریخ انتشار 2013