Life threatening hyperkalemia in a neonate with pseudo-hypoaldosteronism.
نویسندگان
چکیده
Pseudohypoaldosteronism type 1 is a rare disorder characterized by renal resistance to aldosterone which may present with a salt wasting crisis in infancy. We report a neonate with hyponatremia, severe dehydration and refractory life threatening hyperkalemia who was treated with dietary sodium chloride supplementation, potassium binding resins and fluid replacement therapy which proved to be lifesaving.
منابع مشابه
A Neonate with Multiple Causes of Apparent Life-Threatening Event (ALTE): A Case Report
Apparent life-threatening event (ALTE) is a major cause of neonatal emergency visits. In this paper, we presented the case of a three-day-old neonate with multiple indications of ALTE. The patient was referred to the emergency department due to a cyanotic attack before admission. The neonate woke a few hours after breastfeeding and turned blue while crying, which was resolved spontaneously with...
متن کاملPseudohypoaldosteronism in a neonate presenting as life-threatening arrhythmia
UNLABELLED Neonatal hyperkalemia and hyponatremia are medical conditions that require an emergent diagnosis and treatment to avoid morbidity and mortality. Here, we describe the case of a 10-day-old female baby presenting with life-threatening hyperkalemia, hyponatremia, and metabolic acidosis diagnosed as autosomal dominant pseudohypoaldosteronism type 1 (PHA1). This report aims to recognize t...
متن کاملEarly-onset neonatal hyperkalemia associated with maternal hypermagnesemia: a case report
BACKGROUND Neonatal nonoliguric hyperkalemia (NOHK) is a metabolic abnormality that occurs in extremely premature neonates at approximately 24 h after birth and is mainly due to the immature functioning of the sodium (Na+)/potassium (K+) pump. Magnesium sulfate is frequently used in obstetrical practice to prevent preterm labor and to treat preeclampsia; this medication can also cause hypermagn...
متن کاملTransient Pseudohypoaldosteronism due to Urinary Tract Infection in Infancy: A Report of 4 Cases
Hyponatremia with hyperkalemia in infancy is an uncommon but life-threatening occurrence. In the first weeks of life, this scenario is often associated with aldosterone deficiency due to salt-wasting congenital adrenal hyperplasia. However, alternative diagnoses involving inadequate mineralocorticoid secretion or action must be considered, particularly for infants one month of age or older. We ...
متن کاملHyperkalemia due to hyporeninemic hypoaldosteronism with liver cirrhosis and hypertension.
A 49-year-old man with liver cirrhosis and hypertension was found to have hyperkalemia out of a degree of renal insufficiency and metabolic acidosis with low to normal anion gap, aggravated by volume contraction with diarrhea and medications (captopril, spironolactone and atenolol) interfering with potassium homeostasis. Plasma renin activity and serum aldosterone levels of this patient on a re...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- JPMA. The Journal of the Pakistan Medical Association
دوره 62 3 شماره
صفحات -
تاریخ انتشار 2012