Neuronal Ceroid Lipofuscinosis in Australian Merino Sheep
نویسندگان
چکیده
The neuronal ceroid lipofuscinoses (NCLs) are a group of inherited neurodegenerative diseases characterised by the accumulation of autofluorescent lipopigment in a variety of tissues. At least six different forms of NCL occur in humans and the disease has been identified in various animal species, including sheep. Clinical features of NCL are dementia, loss of vision, motor disturbances, and premature death.
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