Relationship of plasma homocysteine with the severity of chronic heart failure.

inherited disease, 7th ed. New York: McGraw-Hill, 1995:791–801. 5. Tanaka K, Orr JC, Isselbacher KJ. The identification of -hydroxyisovaleric acid in the urine of a patient with isovaleric acidemia. Biochem Biophys Acta 1968;152:638–41. 6. Tanaka K, Ikeda Y, Matsubara Y, Hyman D. Molecular basis of isovaleric acidemia in the study of the acyl-CoA dehydrogenase family. Adv Neurol 1988;48:107–31. 7. Truscott RJ, Malegan D, McCairns E, Burke D, Hick L, Sims P, et al. New metabolites in isovaleric acidemia. Clin Chim Acta 1981;110:187–203. 8. Hine DG, Tanaka K. The identification and the excretion pattern of isovaleryl glucoronide in the urine of patients with isovaleric acidemia. Pediatr Res 1984;18:508–13. 9. Lehnert W. Excretion of N-isovalerylglutamic acid in isovaleric acidemia. Clin Chim Acta 1981;116:249–53. 10. Lehnert W. N-Isovalerylalanine and N-isovalerylsarcosine: two new metabolites in isovaleric acidemia. Clin Chim Acta 1983;134:207–12. 11. Millington DS, Roe CR, Maltby DA, Inoue F. Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemia. J Pediatr 1987; 110:56–60. 12. Lehnert W. 3-Hydroxyisoheptanoic acid: a new metabolite in isovaleric acidemia. Clin Chim Acta 1981;113:101–3. 13. Chalmers RA, Lawson AM. Organic acids in man: analytical chemistry, biochemistry and diagnosis of the organic acidurias. New York: Chapman and Hall, 1982:523pp. 14. Duran M, Bruinvis L, Ketting D, Kamerling JP, Wadman SK, Schutgens RBH. The identification of E-2-methylgutaconic acid, a new isoleucine metabolite, in the urine of patients with -ketothiolase deficiency, propionic acidemia and methylmalonic acidemia. Biomed Mass Spectrom 1982;9:1–5. 15. Hagenfeldt L, Naglo AS. New conjugated urinary metabolites in intermediatetype maple syrup urine disease. Clin Chim Acta 1987;169:77–83. 16. Liebich HM, Först C. Urinary excretion of N-acetylamino acids. J Chromatogr 1985;338:187–91. 17. Loots DT, Mienie LJ, Bergh JJ, van der Schyf CJ. Acetyl-L-carnitine prevents total body hydroxyl free radical and uric acid production induced by 1-methyl4-phenyl-1,2,3,6-tetrahydropyridine (MPTP) in the rat. Life Sci 2004;75: 1243–53. 18. Van der Westhuizen FH, Pretorius PJ, Erasmus E. The utilization of alanine, glutamic acid, and serine as amino acid substrates for glycine N-acyltransferase. J Biochem Mol Toxicol 2000;14:102–9.