Nasal Alveolar Rhabdomyosarcoma
نویسندگان
چکیده
Rhabdomyosarcoma is a soft tissue sarcoma arising from cells of myogenic lineage. They can be divided into Embryonal rhabdomyosarcoma (ERMS), Alveolar rhabdomyosarcoma (ARMS) and Pleomorphic rhabdomyosarcoma. ARMS occurs in 10-25years age group and the most common sites being extremities, perirectal and perineal regions, head and neck region is frequently involved in childhood but is exceedingly rare in adults. A female aged about 55years presented in Otolaryngology department with history of left sided nasal obstruction for about 6months. The excised specimen was sent to our Department of Pathology for histopathological examination. ARMS is an aggressive condition and carries a distinctly worse prognosis. We report the case due to the uniqueness of the age and location of the tumor.
منابع مشابه
Nasal Cavity or Alveolar Paranasal Sinus Rhabdomyosarcoma with Orbital Extension in Adults: 2 Cases
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