Schwannomatosis / neurofibromatosis type 2 associated multiple schwannomas visualized on FDG - PET / CT Schwannomatosis / neurofibromatosis tipo 2 en FDG PET / TC de un paciente con múltiples schwannomas
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چکیده
We present a patient with neurocutaneous syndrome, status prior resections for cervical schwannomas and median as well as radial nerve schwannomas. This is a 57-year-old female with neurocutaneous syndrome presenting at 42 years of age with unilateral vestibular schwannoma. Genetic testing was negative but on clinical criteria neurofibromatosis-2 (NF-2) or schwannomatosis were considered.1 She underwent FDG PET/CT 85 min after intravenous injection of 11.3 mCi (418.1 MBq) FDG, for recent onset of severe left back pain with suspected cauda equina compression. Whole-body FDG PET/CT showed multiple FDG avid soft tissue foci overlying the sciatic nerve, consistent with multiple schwannomas (Fig. 1). It also demonstrated heterogenous uptake corresponding to multiple lesions visualized on MRI (Fig. 2).
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A rare case of schwannomatosis
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