Lethal complications of the Ehlers-Danlos syndrome.
نویسنده
چکیده
Death from arterial bleeding or gastrointestinal perforation has previously been reported in more than 15 patients with the Ehlers-Danlos syndrome. On a basis of 100 personally examined patients and a review of published accounts, these events seem particularly likely to occur in two distinct and recognizable forms (the gravis and the ecchymotic forms) of the syndrome.
منابع مشابه
Ehlers-Danlos syndrome: type VI A – kyphoscoliosis; a case report
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ورودعنوان ژورنال:
- British medical journal
دوره 3 5619 شماره
صفحات -
تاریخ انتشار 1968