Hereditary Multiple Gastrointestinal Atresia associated with Choledochal Cyst: A Rare Entity with Management Dilemma
نویسندگان
چکیده
Multiple intestinal atresias are rare and its treatment is challenging. Here, we present a case of multiple gastro-intestinal atresia associated with choledochal cyst posing us a surgical challenge.
منابع مشابه
Extra Hepatic Biliary Atresia Associated with Choledochal Cyst: A Diagnostic Dilemma in Neonatal Obstructive Jaundice
The presentation of extra hepatic biliary-atresia (EHBA) as well as choledochal cyst (CDC) in the neonate may be similar. Since the surgical management and prognosis are entirely different, it is important to differentiate between the two entities. We present a case with co-existing EHBA and CDC which led to a diagnostic dilemma.
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Choledochal cyst is a rare congenital condition, which presents as cystic or fusiform dilatation of the bile duct. The anatomic description and classification scheme for choledochal cystic disease was initially proposed by Alonso-Lej et al., (1959) and later modified by Todani et al.,. The most frequently encountered type is type I cysts, accounting for approximately 85% to 90% of the lesions. ...
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Biliary atresia and choledochal cyst have the similar clinical presentation in infants. Herein, we report a case that presented with prolonged hyperbilirubinemia and abdominal distension and diagnosed as choledochal cyst. At surgery, in addition to a large choledochal cyst, biliary atresia was also encountered.
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