Aneurysmal Fibrous Histiocytoma in Nasal Vestibule Mucosa

Aneurysmal fibrous histiocytoma is a different variant of dermatofibroma, characterized by blood-filled spaces within the fibroblastic tumor. In addition to the typical features of a dermatofibroma, it contains large cleft-like or cavernous blood-filled spaces with numerous hemosiderin pigments. This tumor accounts for less than 2% of all fibrous histiocytomas, and it is typically known to occur in the extremities of middle-aged patients. Clinically, they are larger than cutaneous fibrous histiocytomas in size, may be blue, black, or dark red in color, and may have a cystic consistency. They show symptoms of pain and rapid growth. Knowing the characteristics of this rare lesion is important in terms of the differential diagnosis of other malignant mesenchymal neoplasms. In this article, a case of nasal vestibule skin-induced aneurysmal fibrous histiocytoma has been presented in the literature.