Primary congenital pulmonary hypoplasia of a neonate.

نویسندگان

  • Jui-Sheng Hsu
  • Yu-Sheng Lee
  • Chin-Hsuan Lin
  • Fen-Yau Li
  • Mei-Jy Jeng
  • Wen-Jue Soong
  • Sue-Jen Chen
  • Ren-Bin Tang
چکیده

Pulmonary hypoplasia is a rare but usually lethal disease. We report a full-term male neonate who presented with respiratory failure immediately after birth. Chest X-ray revealed a small lung volume despite advanced ventilator support. Respiratory failure persisted and this baby died at 40.5 hours of age. The autopsy showed a lung-to-birth weight ratio of 0.69% and a radial alveoli count of 2.97. All this information confirmed the diagnosis of primary congenital pulmonary hypoplasia.

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عنوان ژورنال:
  • Journal of the Chinese Medical Association : JCMA

دوره 75 2  شماره 

صفحات  -

تاریخ انتشار 2012