PW03-035 – Autoinflammatory diseases diagnostic chart/tool
نویسندگان
چکیده
Introduction There is great interest in having a reference chart to increase awareness and improve accurate diagnosis for systemic autoinflammatory diseases (SAID), which arealso classical primary immunodeficiency diseases. We have created this wall chart that includes all currently known SAIDs, and arranged the information so that a clinician could compare various symptoms, abnormal labs, genetics, inheritance pattern, affected ethnicity and other information between all of them. In addition, photographs of the main clinical features of many of these diseases have been included to help medical professionals to better understand these diseases, and consider them in the evaluation of candidate patients. As the understanding of autoinflammatory diseases is continuously changing, this chart will probably need to be updated over time. However, the basic information for these diseases will remain helpful for medical professionals.
منابع مشابه
PW03-034 – How to classify autoinflammatory diseases?
Results We propose a clinically-oriented definition: “autoinflammatory diseases are diseases with clinical signs of inflammation, associated with elevated acute phase reactants and due to a dysfunction in the innate immune system, genetically determined or triggered by an endogenous factor”. It is hard to find natural properties able to underlie a useful classification of autoinflammatory disea...
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