Adult onset of multisystem Langerhans cell histiocytosis with skin and lymph node involvement
نویسندگان
چکیده
1Department of Dermatology, Venereology and Allergology, Medical University of Gdansk, Gdansk, Poland Head of the Department: Prof. Roman Nowicki MD, PhD 2Department of Pathology, Medical University of Gdansk, Gdansk, Poland Head of the Department: Prof. Wojciech Biernat MD, PhD 3Department of Oncology and Radiotherapy, Medical University of Gdansk, Gdansk, Poland Head of the Department: Prof. Wojciech Biernat MD, PhD
منابع مشابه
Multisystem Langerhans Cell Histiocytosis in Adult
Langerhans cell histiocytosis (LCH), is a rare disorder, clinically presents with heterogeneous manifestations, and has an unpredictable outcome. Commonly seen in infancy or early childhood, the disorder is characterized by proliferation of abnormal and clonal Langerhans cell in skin, bone, lymph nodes, lungs, liver, spleen, and bone marrow. Occurrence of LCH in adults is rare. Here, we report ...
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We report of a 29-year-old man presented with yellow-red, scaling papules on the skin of scalp, retro-auricular folds, inguinal, axillary, chest and abdomen. The lesions had a poikilodermatious appearance in some areas, such as trunk. The patient also had diabetes insipidus and skull osteolytic lesions. The diagnosis of langerhans cell histiocytosis (LCH) was suggested based on H and E staining...
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