Treatment with cyclosporin A in a patient with Omenn's syndrome.
نویسندگان
چکیده
Unless treated with haematopoetic stem cell transplantation, Omenn's syndrome, a rare variant of severe combined immunodeficiency, is associated with a fatal outcome. We describe a male infant showing all the typical features of Omenn's syndrome, who was successfully treated with cyclosporin A to improve clinical condition prior to haematopoetic stem cell transplantation.
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ورودعنوان ژورنال:
- Archives of disease in childhood
دوره 87 3 شماره
صفحات -
تاریخ انتشار 2002