Prenatal treatment of type I congenital cystic adenomatoid malformation by intrauterine fetal thoracentesis.
نویسندگان
چکیده
Congenital cystic adenomatoid malformation of the lung is a developmental abnormality characterized by abnormal proliferation of terminal bronchioles forming cysts of varying sizes. Extensive lesions are associated with a poor prognosis due to the development of nonimmune hydrops and/or pulmonary hypoplasia. The advent of high-resolution ultrasonography has made it possible to identify these lesions during the antenatal period. With the prenatal identification of cystic adenomatoid malformations comes the potential for in utero intervention to modify the natural history of this process and prevent the development of hydrops and pulmonary hypoplasia. An instance of successful intrauterine treatment of congenital cystic adenomatoid malformation is presented.
منابع مشابه
An unusual prenatal manifestation of a huge congenital cystic adenomatoid malformation with favorable perinatal outcome
Congenital cystic adenomatoid malformation (CCAM) is a rare condition which is easily detectable by prenatal ultrasonography. Fetuses with large CCAMs associating with hydrops are predisposed to perinatal mortality, therefore prenatal intervention is required. While macrocystic CCAM is treated prenatally by thoracentesis or thoraco-amniotic shunt, microcystic or mixed CCAM is difficult to manag...
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CCAM is a rare conolition in the neonatal Period. Two babies were admitted to Mofid hospital with cyanosis and respiratory distress. Pneumectomy was done for both of them for space occupaying lesion. Pathology examination of first case showed area of cuboidal epithelium lined tubes and spaces resembling fetal bronchioles, which are torn in folds. In second case, pathologic examination revealed...
متن کاملFetal MRI as Complementary Study of Congenital Cystic Adenomatoid Malformation During Pregnancy: A Single Case Report
Fetal lung masses are rare findings in prenatal ultrasound scanning in general population, of which congenital cystic adenomatoid malformation is the most commonly diagnosed type. This paper reports a single case of congenital cystic adenomatoid malformation detected at our hospital and the subsequent clinical follow-up using ultrasound scanning and fetal magnetic resonance imaging.
متن کاملIntrauterine therapy in macrocystic type congenital cystic adenomatoid malformation of the lung
Results Mean gestational age at the time of shunt insertion was 25 weeks of gestation. Mediastinal shift were stated in all of the cases. Polyhydramnios was noted in ten fetuses, seven of which were hydropic. In the remaining five fetuses without impaired cardiac function, four had very large lesions (CVR > 1. 6) and one had a lesion that was rapidly increasing in size. Shunt insertion was succ...
متن کاملPrenatal diagnosis and management of congenital cystic adenomatoid malformation.
Congenital cystic adenomatoid malformation (CCAM) is a rare pulmonary malformation resulting from excessive overgrowth of the terminal bronchioles. We present two CCAM case studies: type I (macrocystic) and type III (microcystic), diagnosed by antenatal ultrasonography at 31 and 21 weeks' gestation, respectively. In the former, multiple dilated cystic masses in the fetal left lung, with polyhyd...
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ورودعنوان ژورنال:
- Journal of clinical ultrasound : JCU
دوره 17 9 شماره
صفحات -
تاریخ انتشار 1989