Treatment of diffuse tracheomalacia secondary to relapsing polychondritis with continuous positive airway pressure.
نویسندگان
چکیده
Relapsing polychondritis (RP) is a rare disease characterized by recurrent inflammation and destruction of the cartilaginous structures. Tracheobronchial chondritis is a dreaded complication of RP. We wish to report a case of RP of the trachea and bronchi which was treated with nasal continuous positive airway pressure.
منابع مشابه
Respiratory failure secondary to relapsing polychondritis.
Diffuse airway narrowing of the trachea or main bronchus may result from various autoimmune connective tissue diseases. A careful clinical and pathological evaluation is warranted given the broad differential diagnosis. Relapsing polychondritis (RP) is a rare multisystem disorder that primarily targets cartilaginous structures; however, non-cartilaginous tissue invasion is also seen. Airway inv...
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ورودعنوان ژورنال:
- Chest
دوره 112 6 شماره
صفحات -
تاریخ انتشار 1997