Agenesis of the dorsal pancreas associated with mucinous adenocarcinoma and cystic teratoma: a case report and literature review
نویسندگان
چکیده
Dorsal agenesis of the pancreas is a rare congenital anomaly. Fifty-eight cases were reported from 1913 till 2015, nine of which were associated with tumors. We present the 10th case, the first to be associated with pancreatic mucinous adenocarcinoma and cystic teratoma, successfully managed by Whipple procedure and total pancreatectomy.
منابع مشابه
Cystic Teratoma of the Pancreas
Congenital cystic lesions of the pancreas are rare findings. Furthermore, dermoid cyst of the pancreas is exceptionally uncommon. A review of the world literature showed that only 18 documented cases of dermoid cyst of the pancreas were reported so far. The pre-operative evaluation of this lesion is rather questionable, with definitive diagnosis taking place intra-operatively. Herein, we presen...
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It is presented the case of a 44-year-old woman with ductal adenocarcinoma of the pancreatic head with associated dorsal pancreas agenesis. In this case, curative intent surgery implies removal of the whole pancreas with its consequences--parental insulin requirement and exocrine pancreatic insufficiency. A review of the literature on the previously reported cases was performed.
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CONTEXT Agenesis of the dorsal pancreas is one of the rare congenital malformations of pancreas. The association of agenesis of the dorsal pancreas with pancreatic tumors is extremely rare and only around 9 cases being reported till date. CASE REPORT We report a case of a fifty one year old woman with an agenesis of the dorsal pancreas with periampullary pancreaticobiliary adenocarcinoma. She...
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