Concurrent splenic lymphangiomatosis and Proteus syndrome.
نویسندگان
چکیده
A 37-year-old female presented with Proteus syndrome and was found to have an asymptomatic enlarged spleen. Pathology confirmed splenic lymphangiomatosis. We describe an association of these 2 disorders in the Middle Eastern population. Diagnosis and pathogenesis are discussed in this case report.
منابع مشابه
Lymphangiomas Emmanuel A . Ameh Louise Caouette - Laberge
Combined/complex malformations Klippel-Trenaunay syndrome (capillary-lymphatico-venous malformation) Proteus syndrome Maffucci syndrome Table 110.1: Classification of lymphatic malformations. Introduction Lymphangiomas are developmental defects of the lymphatic channels that belong to a large spectrum of vascular malformations. They are most commonly located in the head and neck region, and to ...
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ورودعنوان ژورنال:
- Saudi medical journal
دوره 34 9 شماره
صفحات -
تاریخ انتشار 2013