Laparoscopic Management of Leiomyoma Developing from Rudimentary Horn in Mayer- Rokitansky- Küster-Hauser Syndrome

Various congenital anomalies of the mullerian system have so far, been described. Our case with MRKH syndrome had two rudimentary horns, and had also a leiomyoma arising from the left rudimentary horn. The patient was presented to our department because of primary amenorrhoea and infertility. Clinical examination revealed a blind vaginal pouch of 3 cm in size and mass was palpated in the left adnexal region measuring about 5 cm in size. At the diagnostic laparoscopy examination, two rudimentary horns were observed to be connected to each other with a fibrous band, and there was a leiomyoma measuring 60 × 50 mm in size originating from the left horn, both of the fallopian tubes and ovaries were normal. The leiomyoma was laparoscopically removed. Using this method have led to successful Clinical outcomes. We sought to present the case of the myoma and its laparoscopic management associated with rarely encountered MRKH syndrome. Although rarely encountered, it should be kept in mind that patients with MRKH syndrome may develop leiomyomas from rudimentary horn. And also laparoscopy is recommended for the diagnosis and treatment of this diseases. about 5 cm in size. Physical examination revealed normal bilateral breasts, normal axillary and pubic hair patterns. Transabdominal ultrasonography showed a solid mass in the left adnexal region. Chromosomal investigation of our case indicated a normal karyotype of 46, XX. Diagnostic laparoscopy revealed that the uterus was absent and there were two rudimentary horns connected with each other by a fibrous band, and there was myoma-like mass 60 x 50 mm arising from the left rudimentary uterine, both ovaries and fallopian tubes were normal in appearance (Figure 1 and Figure 2). The mass was laparoscopically excised. The patient was discharged the following day, histopathological examination confirmed that the mass was a leiomyoma.