Budd-chiari syndrome at diagnosis in polycythemia vera – case report

I. Voican, Universitary Emergency Hospital, Bucharest ABSTRACT Among all BCR-ABL negative chronic myeloproliferative diseases, Polycythemia Vera and Essential Thrombocythemia are most frequently associated with thrombotic events, o en with unusual locations. Hereby we present the case of a patient concomitantly diagnosed with suprahepatic veins thrombosis and PV, where the clinical-pathological picture corroborated with paraclinical data raised the problem of a diff erential diagnosis with Mosse Syndrome. Rapid initiation of an intense cytostatic and anticoagulant treatment, together with pathogenic and symptomatic measures regarding hepatic cirrhosis insured a favorable evolution of the disease, with normalization of hematological parameters, disappearance of phenomenon of liver failure and diminution of the thrombotic process.