Primary Sjö-gren's syndrome presenting with distal, renal tubular acidosis and rhabdomyolysis.

نویسندگان

  • E B S Prakash
  • M E Fernando
  • Malathi Sathiyasekaran
  • R M Bhoopathy
  • J J Jayanth
  • J Samuel
چکیده

Primary Sjögren's syndrome (PSS) is rare in India. Clinically manifest renal disease in PSS is uncommon and is usually an autoimmune tubulointerstitial nephritis presenting with distal renal tubular acidosis (dRTA) or a urinary concentrating defect. Hypokalemic paralysis due to dRTA in PSS is rare but well documented in medical literature. Rhabdomyolysis as a consequence of hypokalemia in PSS is exceptional. We report a case of PSS with dRTA and rhabdomyolysis causing prolonged respiratory failure and quadriparesis.

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عنوان ژورنال:
  • The Journal of the Association of Physicians of India

دوره 54  شماره 

صفحات  -

تاریخ انتشار 2006