Primary hypertrophic osteoarthropathy: case report and literature review
نویسندگان
چکیده
Hypertrophic osteoarthropathy is a pathology characterized by digital clubbing of the hands and feet, extremity enlargement secondary to bone and periarticular tissue proliferation, joint pain and edema, bilateral eyelid ptosis, leonine face and skin thickness.1,2 It is classified as either primary (pachydermoperiostosis) or secondary. The primary form, or idiopathic, is considered rare, corresponding to 3-5% of all cases. Here, we describe the clinical and radiological manifestations of a patient with the primary form of hypertrophic osteoarthropathy, and a literature review about the subject, focusing on the therapeutic challenge of refractory joint pain.
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