Shone's complex with dextrocardia and situs inversus totalis: a case report.

نویسندگان

  • Berkay Ekici
  • Aycan Fahri Erkan
  • Yeliz Sökmen
  • Omaç Tüfekçioğlu
چکیده

Parachute mitral valve complex is an unusual congenital anomaly that has been described by Shone et al. It is characterized by a parachute deformity of the mitral valve associated with additional forms of left heart anomalies, such as aortic valvular stenosis and coarctation of the aorta. A 21-year-old female who was referred to our department because of progressive dyspnea on effort and at rest and minimal cyanosis is presented in this case report. On cardiac auscultation, the patient had a grade III/VI pansystolic murmur best heard at the lower left sternal border. The chest X-ray demonstrated dextrocardia and mild cardiomegaly. Echocardiographic evaluation revealed Shone's complex, including parachute mitral valve anomaly.

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عنوان ژورنال:
  • Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidir

دوره 40 7  شماره 

صفحات  -

تاریخ انتشار 2012