ZEB2 drives immature T-cell lymphoblastic leukaemia development via enhanced tumour-initiating potential and IL-7 receptor signalling

نویسندگان

  • Steven Goossens
  • Enrico Radaelli
  • Odile Blanchet
  • Kaat Durinck
  • Joni Van der Meulen
  • Sofie Peirs
  • Tom Taghon
  • Cedric S. Tremblay
  • Magdaline Costa
  • Morvarid Farhang Ghahremani
  • Jelle De Medts
  • Sonia Bartunkova
  • Katharina Haigh
  • Claire Schwab
  • Natalie Farla
  • Tim Pieters
  • Filip Matthijssens
  • Nadine Van Roy
  • J. Adam Best
  • Kim Deswarte
  • Pieter Bogaert
  • Catherine Carmichael
  • Adam Rickard
  • Santi Suryani
  • Lauryn S. Bracken
  • Raed Alserihi
  • Kirsten Canté-Barrett
  • Lieven Haenebalcke
  • Emmanuelle Clappier
  • Pieter Rondou
  • Karolina Slowicka
  • Danny Huylebroeck
  • Ananda W. Goldrath
  • Viktor Janzen
  • Matthew P. McCormack
  • Richard B. Lock
  • David J. Curtis
  • Christine Harrison
  • Geert Berx
  • Frank Speleman
  • Jules P. P. Meijerink
  • Jean Soulier
  • Pieter Van Vlierberghe
  • Jody J. Haigh
چکیده

Early T-cell precursor leukaemia (ETP-ALL) is a high-risk subtype of human leukaemia that is poorly understood at the molecular level. Here we report translocations targeting the zinc finger E-box-binding transcription factor ZEB2 as a recurrent genetic lesion in immature/ETP-ALL. Using a conditional gain-of-function mouse model, we demonstrate that sustained Zeb2 expression initiates T-cell leukaemia. Moreover, Zeb2-driven mouse leukaemia exhibit some features of the human immature/ETP-ALL gene expression signature, as well as an enhanced leukaemia-initiation potential and activated Janus kinase (JAK)/signal transducers and activators of transcription (STAT) signalling through transcriptional activation of IL7R. This study reveals ZEB2 as an oncogene in the biology of immature/ETP-ALL and paves the way towards pre-clinical studies of novel compounds for the treatment of this aggressive subtype of human T-ALL using our Zeb2-driven mouse model.

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عنوان ژورنال:

دوره 6  شماره 

صفحات  -

تاریخ انتشار 2015