[Acute postinfectious pityriasis rubra pilaris: a superantigen-mediated dermatosis].

نویسندگان

  • C Ferrándiz-Pulido
  • R Bartralot
  • P Bassas
  • D Bodet
  • T Repiso
  • G Aparicio
  • J Mollet
  • M Serra
  • V García-Patos
چکیده

Acute postinfectious pityriasis rubra pilaris (PRP) is a variant of juvenile PRP (Griffiths type III) characterized by no family history, an acute course associated with a prior fever, and good prognosis. Clinical features may resemble other superantigen-mediated diseases, such as scarlatiniform rash or staphylococcal scalded skin syndrome, but its histology and treatment are different. We present 4 cases of acute postinfectious PRP that illustrate the clinical features of this uncommon disease and we review possible underlying pathogenic mechanisms.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Pityriasis rubra pilaris: evolution of challenges in promising treatment options.

Pityriasis rubra pilaris is an uncommon inflammatory dermatosis that is well recognized across the globe. Erythroderma is a common presentation. A precise diagnosis of pityriasis rubra pilaris is based on morphologic features and is classified into 6 types: classic adult onset (type I), atypical adult (type II), classic juvenile (type III), circumscribed juvenile (type IV), atypical juvenile (t...

متن کامل

Successful treatment of type II pityriasis rubra pilaris with secukinumab

IL: interleukin PRP: pityriasis rubra pilaris TNF: tumor necrosis factor INTRODUCTION Pityriasis rubra pilaris (PRP) is a heterogeneous inflammatory skin disease characterized by follicular papules, orange palmoplantar keratoderma, and erythematous scaly patches with islands of skin sparing. Type II PRP is a rare, severe, chronic form of PRP presenting atypical features including long disease d...

متن کامل

Case Report Circumscribed juvenile pityriasis rubra pilaris

Pityriasis rubra pilaris (PRP) is an uncommon papulosquamous inflammatory dermatosis of unclear aetiology. Its most remarkable clinical findings are palmoplantar hyperkeratosis, orange-red scaling plaques and hyperkeratotic follicular papules. Its extension may vary from localised subtypes to generalised skin involvement with well-demarcated areas of spared skin ("islands of sparing") to erythr...

متن کامل

Pityriasis rubra pilaris presenting with an abnormal autoimmune profile: two case reports

INTRODUCTION Pityriasis rubra pilaris is an uncommon inflammatory and hyperproliferative dermatosis of juvenile or adult onset. The etiology of the disease is still unknown. CASE PRESENTATION We present the cases of two Caucasian men aged 53 and 48 who presented with pityriasis rubra pillaris type 1; both patients also exhibited an abnormal immunological profile. CONCLUSION Pityriasis rubra...

متن کامل

Etanercept-induced clinical remission of type II pityriasis rubra pilaris with rheumatoid arthritis.

Pityriasis rubra pilaris (PRP) is a rare papulosquamous dermatosis characterized by keratotic follicular papules, erythematous scaling, pahnoplantar keratoderma and a variable degree of erythroderma. Type I PRP, the most common adult form, has a typical clinical manifestation, and remission in these patients can be achieved within 3 years. However, the rare type II PRP presents atypical feature...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • Actas dermo-sifiliograficas

دوره 100 8  شماره 

صفحات  -

تاریخ انتشار 2009