Intercurrent illness in inborn errors of intermediary metabolism.

نویسندگان

  • M A Dixon
  • J V Leonard
چکیده

Metabolic decompensation may occur in patients with disorders of intermediary metabolism during intercurrent illness. To prevent complications it is normal practice to change the diet to an 'emergency regimen'. The mainstay of this is a high carbohydrate intake, using soluble glucose polymer, given as frequent drinks by day and during the night. Additional therapy is given for some disorders. Practical details of the treatment are outlined.

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عنوان ژورنال:
  • Archives of disease in childhood

دوره 67 11  شماره 

صفحات  -

تاریخ انتشار 1992