Catastrophic Primary Antiphospholipid Syndrome
نویسندگان
چکیده
drome (APLS) may present with a catastrophic condition characterized by multiple vascular occlusions that often result in death if appropriate treatment is not quickly applied. In the great majority of cases, patients with catastrophic APLS show a spontaneous tendency to develop microvascular thrombosis that affects multiple organs. However, arterial reactivity leading to acute thrombosis after operation or a procedure has rarely been reported on (1, 2). We report here on a case characterized by a succession of thrombotic accidents that occurred during or immediately after arterial angiographies or arterial surgery, and catastrophic arterial reactivity was strongly suspected.
منابع مشابه
The Flare Up of Catastrophic Antiphospholipid Syndrome: a Report of an Immunosuppressive Withdrawal-Induced Case
Antiphospholipid syndrome (APS) is a systemic disease that causes venous and arterial thrombosis in virtually any organ. Sometimes it is complicated into pulmonary infarction and cavitation, pulmonary hypertension, and catastrophic course with high morbidity and mortality. The present case is a 35-year-old woman with one episode of postpartum deep veins throm-bosis (DVT) 12 years earlier and th...
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logic correlations of the antiphospholipid syndrome. Semin Arthritis Rheum 1995; 24:262-72. 2 Asherson RA. The catastrophic antiphospholipid syndrome. J Rheumatol 1992;19:508-12. 3 Asherson RA, Piette J-C. The catastrophic antiphospholipid syndrome 1996: acute multiorgan failure associated with antiphospholipid antibodies: a review of 31 patients. Lupus 1996;5:414-7. 4 Mazzucchelli R, Barbadill...
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