Living-donor liver transplant in 3 patients with Budd-Chiari syndrome: case report.

نویسندگان

  • Koray Bas
  • Onur Yaprak
  • Murat Dayangac
  • Onur Levent Ulusoy
  • Gulen Bulbul Dogusoy
  • Yildiray Yuzer
  • Yaman Tokat
چکیده

Budd-Chiari syndrome is a rare but life-threatening disorder characterized by obstruction of the hepatic venous outflow. Treatment depends on the underlying cause, the location, and extent of the obstruction, and the functional capacity of the liver. A stepwise therapeutic approach is commonly accepted. When all other therapy options are unsuccessful, or in case of end-stage liver disease, transplant should be considered. We present case reports of 3 patients with Budd-Chiari syndrome who underwent living-donor liver transplant. Characteristic features of Budd-Chiari syndrome, diagnostic and therapeutic interventions, complications, and overall outcomes are discussed. We believe that when a deceased donor graft is unavailable, a living-donor liver transplant can be a safe option for patients with end-stage liver disease associated with Budd-Chiari syndrome.

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عنوان ژورنال:
  • Experimental and clinical transplantation : official journal of the Middle East Society for Organ Transplantation

دوره 10 2  شماره 

صفحات  -

تاریخ انتشار 2012