Anterior lenticonus and Alport's syndrome.
نویسندگان
چکیده
A case of anterior lenticonus is reported in a 26 year old man with hemorrhagic nephritis related to familial Alport's syndrome. Anterior lenticonus is seen only as a part of Alport's syndrome. The authors describe its clinical, histologic and therapeutic aspects. They also discuss the other ocular manifestations, the nephritis and the sensorineural deafness.
منابع مشابه
Alport's syndrome: case report and review of ocular manifestations.
A 66-year-old man with the classic signs of Alport's syndrome--progressive hemorrhagic nephropathy and sensorineural deafness--plus bilateral anterior lenticonus, anterior and posterior subcapsular cataracts, and scattered lens opacities is presented. Bilateral anterior leniconus is rarely seen in patients without the syndrome. The syndrome is usually fatal in males by the second or third decad...
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Alport's syndrome is characterised by progressive haematuric nephritis and high tone sensorineural hearing loss. Ocular signs are variable, the most consistent findings being anterior lenticonus and retinal flecks in the macula and mid peripheral areas. Previous electrophysiological studies on patients with Alport's syndrome have mostly been on adult patients undergoing haemodialysis, or after ...
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OBJECTIVE We describe a simplified method to detect anterior lenticonus. Three eyes of 2 patients with anterior lenticonus, plus 16 eyes from 16 healthy controls underwent Scheimpflug imaging of their anterior segment with Pentacam. The anterior capsule apex angle was manually identified and automatically measured by AutoCAD. RESULTS The mean angle was 173.06° (SD: 1.91) in healthy subjects, ...
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ورودعنوان ژورنال:
- The British journal of ophthalmology
دوره 50 7 شماره
صفحات -
تاریخ انتشار 1966