Prophylactic Treatments for Retinal Tears/Detachment in Stickler Syndrome: Single Institution Experience
نویسندگان
چکیده
Background: To report the clinical features and prophylactic treatment methods for retinal pathology in Stickler syndrome (SS) patients (pts). Methods: A retrospective non-comparative interventional case series. Results: The median age of the pts was 12 (range 0.2-68) years. Systemic features of SS were present in 23 pts. High myopia was present in 19 pts. Treatment was by laser retinopexy and or cryotherapy (n=15) and vitrectomy plus scleral buckle (SB) (n=6). Five fellow eyes with extensive lattice degeneration with or without associated retinal tears treated by prophylactic SB. The median follow-up was 65.5 months (range 5-226). Seven fellow eyes developed RD over a median duration of 22.5 (range 5-123) months, who were treated by vitrectomy plus SB (n=6) and vitrectomy, silicon oil and laser retinopexy (n=1). Conclusions: Prophylactic treatments such scleral buckle and laser and cryotherapy prevented the development of retinal tears or detachment in pts with Stickler syndrome.
منابع مشابه
Retinal detachment and prophylaxis in type 1 Stickler syndrome.
PURPOSE To report the prevalence of retinal detachment (RD) and results of prophylaxis against detachment from a giant retinal tear in a large cohort of patients with type 1 Stickler syndrome. DESIGN Retrospective study. PARTICIPANTS Two hundred four type 1 Stickler syndrome patients. METHOD Pedigrees and individuals with type 1 Stickler syndrome were identified from the vitreous research...
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