G6PD deficiency in two autochthonous Croatian families.

In Europe G6PD deficiency is encountered most frequently in Sardinia and Greece but may also be found in other Mediterranean countries (Sansone, Piga, and Segni, 1958; Szeinberg, Asher, and Sheba, 1958), including Yugoslavia (Fraser, Grunwald, and Stamatoyannopoulos, 1966). The occurrence of haemolytic anaemia after ingestion of fava beans in Yugoslavia was first reported as a clinical finding by Vince-Ribaric in 1962. The patients belonged to two autochthonous Croatian families from the vicinity of the town of Zadar on the Adriatic Coast. In the present study a full account is given of all the data obtained in the patients and their families.