Pearls & Oy-sters: Tonic eye deviation in stiff-person syndrome.

نویسندگان

  • Sudheer Chakravarthi
  • Manoj Kumar Goyal
  • Vivek Lal
چکیده

1. Stiff-person syndrome (SPS) is an autoimmune disease characterized by muscle rigidity, episodic muscle spasms, as well as continuous cocontraction of agonist and antagonist muscles. 2. Although a criterion for diagnosis of SPS, anti– glutamic acid decarboxylase (anti-GAD) antibodies can be negative in up to 40% of patients. In absence of antibodies, characteristic EMG findings of continuous motor unit activity and decrease in this activity with diazepam are helpful in diagnosis.

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عنوان ژورنال:
  • Neurology

دوره 84 17  شماره 

صفحات  -

تاریخ انتشار 2015