Anesthetic management of a patient with congenital insensitivity to pain: a case report.
نویسنده
چکیده
Pain protects the body from damaging effects of harmful stimuli. Congenital insensitivity to pain is a rare inherited disorder characterized by diminished or absent sensitivity to pain, touch, and pressure that leads to frequent trauma and self-mutilation. The disorder is part of the hereditary sensory and autonomic neuropathy (HSAN) family, in which 5 types have been recognized. Research and case reports of anesthetic risks and analgesic needs of these patients is limited due to the infrequent nature of the disorder. Recommendations for anesthesia include modification of intraoperative opioid requirements, use of anesthetics to ensure cooperation and immobility, and intraoperative temperature monitoring. It is imperative for anesthesia providers to understand which type of HSAN their patient experiences and to conduct a thorough preoperative interview because a different interpretation of sensory loss may occur in each HSAN category. This article reports the case of a patient with HSAN type 2 who presented for knee arthroscopy.
منابع مشابه
Congenital Insensitivity to Pain with Anhidrosis in an Iranian Patient
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متن کامل[Anesthesia in a patient with congenital insensitivity to pain and anhidrosis].
BACKGROUND AND OBJECTIVES Congenital insensitivity to pain and Anhidrosis (CIPA) or hereditary sensory and autonomic neuropathy type IV (HSAN IV) is a rare autosomal recessive neuropathy of the group of hereditary sensory and autonomic neuropathies (HSAN) characterized by insensitivity to pain, anhidrosis, and mental retardation. Since it is a rare condition, reports on the anesthetic conduct i...
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ورودعنوان ژورنال:
- AANA journal
دوره 81 5 شماره
صفحات -
تاریخ انتشار 2013