Lymphoproliferative disease and acquired C1 inhibitor deficiency.
نویسندگان
چکیده
Angioedema due to acquired deficiency of the C1-inhibitor is a bridging condition between autoimmunity and lymphoproliferation. We report 32 patients with acquired C1 inhibitor deficiency: 23 have anti C1-inhibitor autoantibodies; 13 have monoclonal gammopathies of unknown significance and 9 have non-Hodgkin's lymphoma. Our series suggest that different forms of B cell disorders coexist and/or evolve into each other in acquired angioedema.
منابع مشابه
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ورودعنوان ژورنال:
- Haematologica
دوره 92 5 شماره
صفحات -
تاریخ انتشار 2007