Sinus Histiocytosis with Massive Lymphadenopathy – Its Rare Immunological Complication
نویسندگان
چکیده
Sinus histiocytosis with massive lymphadenopathy (SHML) is a nonneoplastic, usually self limiting disease of unknown aetiology [1]. SHML most commonly presents as painless cervical lymphadenopathy with frequent involvement of other lymph nodes. In 30% of patients extranodal sites such as skin, bone, eye, and breast are involved [2]. Evidence of various immunological dysfunctions has also been documented in few case studies [3]. The authors report here one uncommon interesting case of generalised lymphadenopathy with autoimmune haemolytic anaemia.
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