Splenomegaly and hepatomegaly in an adolescent simulating Banti's syndrome.
نویسندگان
چکیده
Banti's disease, or Banti's syndrome as it is now generally called, is really a symptom complex, characterized by splenomegaly, and a progressive anaemia, with a tendency to gastro-oesophageal haemorrhage, and often accompanied by some degree of hepatic involvement. In Banti's description of the condition, he distinguished three stages:(1) Splenomegaly with an associated secondary anaemia. (2) A short transitional stage with hepatic enlargement and jaundice. (3) A terminal stage characterized by cirrhosis of the liver and ascites. The case described exhibited many of the above phenomena.
منابع مشابه
Banti's syndrome: case report and review of literature.
In 1898 Banti described a disorder characterized by splenomegaly and hypersplenism, resulting in portal hypertension and anemia in the absence of hematological disease. 1 Banti's syndrome is also known as non-cirrhotic portal hypertension (NCPH) in India and Idiopathic Portal Hypertension (IPH) in Japan. Hepatoportal sclerosis seems to be its counterpart in the United States. 2,3 Banti's syndro...
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ورودعنوان ژورنال:
- Archives of disease in childhood
دوره 20 103 شماره
صفحات -
تاریخ انتشار 1945