Banti's syndrome in childhood: A report of four cases.

نویسنده

  • L C Martin
چکیده

Haematemesis in childhood is a rare event which may be due to similar causes to those occurring in adults, barring malignant disease. After the age of infancy the commonest disorder in which it is found is splenic anaemia or Banti's disease. The distinction between those two conditions is ill (lefined; they are commonly regarded as synonymous and either diagnosis is applied to a case exhibiting splenomegaly and anaemia of obscure origin, with or without haemorrhages, hepatic cirrhosis or ascites.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Report of a four-year-old boy with Progeria without total Alopecia

Hutchinson-Gilford progeria syndrome is an extremely rare condition with features of premature and accelerated aging. The pattern of inheritance is unclear, although autosomal dominant mutations have been proposed. The disease presentation is usually in infancy and early childhood with a characteristic phenotype of short stature, abnormal skin and nail, beaked nose, loss of subcutaneous f...

متن کامل

Splenomegaly and hepatomegaly in an adolescent simulating Banti's syndrome.

Banti's disease, or Banti's syndrome as it is now generally called, is really a symptom complex, characterized by splenomegaly, and a progressive anaemia, with a tendency to gastro-oesophageal haemorrhage, and often accompanied by some degree of hepatic involvement. In Banti's description of the condition, he distinguished three stages:(1) Splenomegaly with an associated secondary anaemia. (2) ...

متن کامل

Wiskott-Aldrich Syndrome (WAS): A Case Report in Mauritius and Review

Wiskott-Aldrich is an X-lined recessive disorder typically characterized by thrombocytopenia, eczema and recurrent infections. We report the four year treatment progress of a six year old boy who initially presented with vesicular lesions over the trunk, upper and lower extremities and face and blood tinged stools at the age of 2 weeks. From the family pedigree, there were two suspected cases t...

متن کامل

Childhood Pemphigus: Report of 2 cases

Pemphigus is rare in children, only 71 cases have been reported in literature. We report 2 cases of pemphigus vulgaris (13 and 15 years old) among 147 cases of pemphigus from Khouzestan who were admitted to the Department of Dermatology, Ahwaz Medical University between 1989-2001. The basis of diagnosis was clinical and histopathological findings in each patient. One patient was treated only wi...

متن کامل

Banti's syndrome: case report and review of literature.

In 1898 Banti described a disorder characterized by splenomegaly and hypersplenism, resulting in portal hypertension and anemia in the absence of hematological disease. 1 Banti's syndrome is also known as non-cirrhotic portal hypertension (NCPH) in India and Idiopathic Portal Hypertension (IPH) in Japan. Hepatoportal sclerosis seems to be its counterpart in the United States. 2,3 Banti's syndro...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • Archives of disease in childhood

دوره 11 65  شماره 

صفحات  -

تاریخ انتشار 1936