A Congenital Gerbode Defect associated with a Rare Structural Abnormality of the Mitral Valve Diagnosed in an Adult Patient

نویسندگان

  • Anca D. Mateescu
  • Ioan M. Coman
  • Carmen C. Beladan
  • Bogdan Radulescu
  • Carmen Ginghina
  • Bogdan A. Popescu
چکیده

We report the case of a rare association of a congenital Gerbode defect with severe mitral regurgitation due to abnormal linear structure of mitral valve, diagnosed in an adult patient. The case highlights the importance of a thorough examination interpreting the echocardiographic findings on a pathophysiological basis. It also underlines the complementary role of different imaging techniques with transesophageal echocardiography, allowing the precise assessment of both structural and functional abnormalities in such a complex case. The patient underwent mitral valve replacement with a bileaflet mechanical prosthesis and repair of the Gerbode defect. The imaging findings were confirmed during the surgical procedure, leading to a good outcome.

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عنوان ژورنال:

دوره 46  شماره 

صفحات  -

تاریخ انتشار 2016