Marfanoid hypermobility syndrome associated with coarctation of the aorta.

نویسندگان

  • A Daneshwar
  • D Tavakoli
  • J Nazarian
چکیده

There are intimate interrelations between various elements of connective tissue, viz. collagen, elastin, and glycoproteins. It is not unexpected that Marfan and Ehlers-Danlos syndromes share common features. The condition is labelled as Marfanoid hypermobility syndrome. In the patient described here, the Marfanoid hypermobility syndrome was associated with coarctation of the aorta which was corrected surgically.

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570 Indian Journal of Dermatology 2016; 61(5) 7. Walker BA, Beighton PH, Murdoch JL. The Marfanoid hypermobility syndrome. Ann Intern Med 1969;71:349-52. 8. Daneshwar A, Tavakoli D, Nazarian J. Marfanoid hypermobility syndrome associated with coarctation of the aorta. Br Heart J 1979;41:621-3. 9. Terada Y, Wanibuchi Y. Surgically treated case of Marfanoid hypermobility syndrome. Ann Thorac Surg...

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عنوان ژورنال:
  • British heart journal

دوره 41 5  شماره 

صفحات  -

تاریخ انتشار 1979