Clinical application of Nuss procedure for chest wall deformity in Poland syndrome
نویسندگان
چکیده
A 6-year-old girl with Poland syndrome was diagnosed with loss of hard and soft tissue on her affected chest. She required chest reconstruction to protect her thorax and improve her developmental delay. We applied a titanium device used for children with funnel chest to her, resulting in good shape. By using this device, we avoided sacrificing healthy rib and muscle; she could save the tissue for secondary surgery in puberty. The device made it possible to support the growth of her thoracic frame and has kept it in good shape. Also, 66 months after removing the device, her chest contour has been maintained. We evaluated the change of her chest frame by comparing the preoperative and postoperative CT index and found the result quite an improvement. We suggest that our technique would be easy, of low invasiveness, and safe for treatment of thoracic deformity in school age.
منابع مشابه
First Iranian Experience of the Minimally Invasive Nuss Procedure for Pectus Excavatum Repair: A Case Series and Literature Review
Pectus excavatum is the most common congenital deformity of the chest wall. The most frequently used techniques include Ravitch (costochondral resection) and Nuss (minimally invasive pectus repair of pectus excavatum [MIRPE]). The Nuss technique includes using temporary metallic bars without costochondral resection to correct the chest wall deformity. Modified MIRPE can be learned easily and pe...
متن کاملComments on the article “Clinical application of Nuss procedure for chest wall deformity in Poland syndrome”
Poland’s syndrome is a very rare type of chest deformation found in 1 : 32,000 – 1 : 52,500 live births [1, 2]. Its treatment most often involves the reconstruction of the mammary glands with the transposition of a pedicled muscle-skin flap using Marlex mesh [3, 4] or the repair of the chest’s bone structure. The coexistence of multiple developmental defects of the chest constituting this syndr...
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OBJECTIVE In 1998, Dr Donald Nuss proposed minimally invasive repair of pectus excavatum (MIRPE) which did not require the osteochondrous parts of the anterior chest wall to be resected. The paper aims at presenting the authors' own 6 years of experience in funnel chest repair with MIRPE technique. Also, many technical problems of this method are discussed. MATERIALS AND METHODS Between 1999 ...
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Pectus excavatum is a deformity of the thoracic wall present in less than 1% of the population. Treatment is essentially surgical because of the size of the deformity. The most employed surgical options are the technique proposed by Ravitch and its variations and the technique proposed by Nuss. The first one is considered the conventional technique, while the Nuss procedure is minimally invasiv...
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