Guidelines on the diagnosis and management of thrombotic thrombocytopenic purpura and other thrombotic microangiopathies.

نویسندگان

  • Marie Scully
  • Beverley J Hunt
  • Sylvia Benjamin
  • Ri Liesner
  • Peter Rose
  • Flora Peyvandi
  • Betty Cheung
  • Samuel J Machin
چکیده

Marie Scully, Beverley J. Hunt, Sylvia Benjamin, Ri Liesner, Peter Rose, Flora Peyvandi, Betty Cheung and Samuel J. Machin on behalf of British Committee for Standards in Haematology Department of Haematology, UCLH, London, Department of Haematology, King’s College and Guys &St Thomas’ NHS Trust, London, Department of Haematology, NBSBT and Oxford University Hospitals (OUH) Trust, UK, Department of Haematology, GOSH, London, Department of Haematology, University Hospitals Coventry &Warwickshire NHS trust, Coventry, UK, Department of Haematology, IRCCS Maggiore Hospital Ca’ Granda Foundation, University of Milan, Milan, Italy, Department of Haematology, Queen Elizabeth Hospital, SLHT, London and Department of Haematology, UCL, London, UK

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Thrombotic Thrombocytopenic Purpura: Diagnosis and Treatment

Thrombotic Thrombocytopenic purpura (TTP) is a rare thrombotic microangiopathic disease, associated with thrombocytopenia and hemolytic anemia. It is caused by an enzymatic dysfunction responsible in cleavage of blood clotting factors. In this study we have tried to review the available approaches in diagnoses of the disease as well as treatment strategies. Based on the what the current review ...

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Thromb Haemost 2005;3:1432-6. 4. Dashe JS, Ramin SM, Cunningham FG. The long-term consequences of thrombotic microangiopathy (thrombotic thrombocytopenic purpura and hemolytic uremic syndrome) in pregnancy. Obstet Gynecol 1998;91:662-8. 5. Miner PE, Nutt RL, Thomas ME. Thrombotic thrombocytopenic purpura occurring in pregnancy. Am J Obstet Gynecol 1955;70:611-7. 6. Weiner CP. Thrombotic microan...

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Successful treatment of thrombotic thrombocytopenic purpura during pregnancy: A case report

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عنوان ژورنال:
  • British journal of haematology

دوره 158 3  شماره 

صفحات  -

تاریخ انتشار 2012