Epidermolytic hyperkeratosis with a rare digital contracture.
نویسندگان
چکیده
A sixteen year-old male patient with no history of consanguinity in the family, reported with patchy, thickened lichenified plaques over the whole body. Some areas had normal skin while some were Blaschkoid lesions. The child had delayed milestones along with hypogonadism. Digital contracture with palmoplantar keratoderma was present. Histopathology showed characteristic vacuolar degeneration of the upper epidermis and suprabasilar keratinocytes with hyperkeratosis.
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ورودعنوان ژورنال:
- Indian journal of dermatology, venereology and leprology
دوره 73 4 شماره
صفحات -
تاریخ انتشار 2007