[Bilateral pulmonary veins atresia].

Rev Esp Cardiol 2002;55(6):671-2 671 Congenital atresia of the pulmonary veins is a rare anomaly that is not associated with other heart disease. It has a poor prognosis and patients die secondary to pulmonary hypertension, recurrent hemoptysis, pulmonary edema, or congestive cardiac insufficiency. We present a 5-year-old male patient admitted to the hospital for asthenia, anorexia, hemoptoic vomiting, and a severe cough. Marked dystrophy was observed, with a weight of less than the 3rd percentile, pale skin and mucous, and bilateral nystagmus. Cardiovascular examination did not reveal murmurs and the second heart sound was strong. With respect to echocardiogram data, on 4-chamber projection the connections of the left pulmonary veins and the right superior vein lobe to the left atrium were not seen; in the short axis projection the great vessels were in a normal relationship, with the diameter of the pulmonary artery being greater than the diameter of the ascending aorta, the IM AG E S I N C A R D I O L O G Y