Sirenomelia Associated with Truncus Arteriosus
نویسندگان
چکیده
Syrenomelia sequence is a rare (incidence of 1: 60000 births) [1,2] lethal pattern of congenital anomalies characterized by a number of hallmark skeletal anomalies including fusion of the lower extremities or a single lower limb, bilateral renal agenesis or dysgenesis with absent or hypoplastic renal arteries, oligohydramnios and the presence of aberrant vasculature. Prenatal sonographic detection of the lower limb anomalies associated with this condition is severely limited by the oligohydramnios that accompanies bilateral renal agenesis.
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