Floating Lens In Marfan’s Syndrome: A Case Report

نویسندگان

  • Jaideep Bhatt
  • Pankaj Kumar
چکیده

Marfan’s syndrome (MFS) is an autosomal dominant connective tissue disorder involving the cardiovascular, skeletal and ocular systems.Cardinal manifestations include aortic aneurysm and dissection, ocular lens dislocation and long bone overgrowth. The most common cause of ectopia lentis is trauma, which accounts for nearly onehalf of all cases of lens dislocation. A forward dislocation of the lens into the pupil or anterior chamber may cause pupillary block with acute glaucoma or chronic angle-closure glaucoma. Posterior dislocation can cause harmful vitreous traction on the retina with leakage of lens proteins into the vitreous, which may cause chronic vitritis and chorioretinal inflammation. We presented a case of Marfan’s syndrome who presented with anterior dislocated lens in sitting posture which falls back to posterior segment in supine position which we described it as “floating lens” which has not been described in medical literature so far. Surprisingly, when the dislocated lens was in the anterior chamber, IOP was unrecordably low in contrast to what’s expected in literature (IOP is always raised in anteriorly dislocated lens of Marfan’s syndrome due to pupillary block)

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تاریخ انتشار 2015