Prevalence of monogenic autoinflammatory diseases among Pediatric Rheumatology centers: the Eurofever PReS/PRINTO survey
نویسندگان
چکیده
Address: 1UO Pediatria II, Istituto Gaslini and Dipartimento di Pediatria, Università di Genova, Genova, Italy, 2University Medical Center, Utrecht, Utrecht, Italy, 3Hacettepe University Faculty of Medicine, Ankara, Turkey, 4Bambino Gesù Pediatric Hospital, Roma, Italy, 5Centre HospitaloUniversitaire de Bicêtre, Le Kremlin Bicêtre, France, 6Hopital Necker-Enfants Malades, Paris, France, 7University of Würzburg, Würzburg, Germany, 8University of Istanbul, Cerrahpaşa Medical Faculty, Istanbul, Turkey, 9Universitair Ziekenhuis Leuven, Leuven, Belgium, 10University College London, London, UK, 11Centre Hospitalier Universitaire Vaudois, Lausanne, Switzerland, 12Department of Paediatrics, Charles University, Prague, Czech Republic, 13Department of Rheumatology University Children's Hospital, Ljubljana, Slovenia and 14Faculty Children's Hospital 1st Department for Children and Adolescents, Kosice, Slovakia * Corresponding author
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PReS-FINAL-2329: Validation of the autoinflammatory activity index (AIDAI)
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Methods A web-based registry collecting baseline and clinical information of autoinflammatory diseases was located at the member area of the PRINTO website (www.printo. it). Participating hospitals included pediatric rheumatology centers of the PRINTO network and adult centers with a specific interest in autoinflammatory diseases. Data was collected on Blau’s syndrome, Behçet’s disease, CAPS, C...
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