Familial diffuse progressive encephalopathy.
نویسندگان
چکیده
The purpose of this paper is to present the clinical and neuropathological findings in two idiot brothers in whom the mode and time of onset and the pattern of brain anomalies were remarkably similar. Clinically there were similarities with well-known syndromes such as Tay Sachs and Schilder's disease. However, the ultimate diagnosis was to emphasize the frequent difficulties encountered in determining the aetiology of mental deficiency with progressive neurological features.
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ورودعنوان ژورنال:
- Archives of disease in childhood
دوره 35 شماره
صفحات -
تاریخ انتشار 1960